| Mutation type:Point | Mutation effect:Missense | Nucleotide number:316 | |||
| Genome location:Exon5 | Subdomain:EGF1 | ||||
| Alpha missense prediction value:0.8642 | Alpha missense prediction class:pathogenic | ||||
| No. of patients reported: 7 | |||||
| Patient information: Monoallelic variation (7); Biallelic variation (0) | |||||
| Patient | Sex | Age | Genotype | PC: amidolytic act (%) | PC: clotting act (%) | PC: Ag (%) | PCD type | Clinical presentation (age) | First onset age | Country | Comments | Reference |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | M | 22 | hetero | 47 | 39 | 53 | I | DVT (20) | 20 | Poland | Dabigatran | PMID: 35627118 |
| 2 | F | 48 | hetero | 46 | 34 | 35 | I | DVT (45); PE | 45 | Poland | Apixaban | PMID: 35627118 |
| 3 | M | 29 | hetero | 42 | NA | 44 | I | DVT, PE (29), recurrence Other VTE | 29 | Poland | NA | PMID: 28607330 |
| 4 | M | 37 | hetero | 51 | NA | 65.5 | I | DVT, PE (37) | 37 | Poland | NA | PMID: 28607330 |
| 5 | F | 22 | hetero | 42.4 | NA | NA | I | DVT (20), Other VTE | 20 | Poland | NA | PMID: 28607330 |
| 6 | M | 26 | hetero | 48 | NA | 44.9 | I | asymptomatic | 26 | Poland | family history of VTE | PMID: 28607330 |
| 7 | M | 29 | hetero | 42 | NA | 44 | I | DVT, PE with hypotonia (29) | 29 | Poland | anticoagulation therapy, tenecteplase, enoxaparin. | PMID: 24496376 |
| Mutation type:Point | Mutation effect:Missense | Nucleotide number:316 | |||
| Genome location:Exon5 | Subdomain:EGF1 | ||||
| Alpha missense prediction value:0.6965 | Alpha missense prediction class:pathogenic | ||||
| No. of patients reported: 1 | |||||
| Patient information: Monoallelic variation (1); Biallelic variation (0) | |||||
| Patient | Sex | Age | Genotype | PC: amidolytic act (%) | PC: clotting act (%) | PC: Ag (%) | PCD type | Clinical presentation (age) | First onset age | Country | Comments | Reference |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | NA | 46 | hetero | 44.1 | NA | 53.3 | I | DVT | 46 | China | NA | PMID: 22545135 |
| Mutation type:Point | Mutation effect:Missense | Nucleotide number:316 | |||
| Genome location:Exon5 | Subdomain:EGF1 | ||||
| Alpha missense prediction value:0.6965 | Alpha missense prediction class:pathogenic | ||||
| No. of patients reported: 1 | |||||
| Patient information: Monoallelic variation (1); Biallelic variation (0) | |||||
| Patient | Sex | Age | Genotype | PC: amidolytic act (%) | PC: clotting act (%) | PC: Ag (%) | PCD type | Clinical presentation (age) | First onset age | Country | Comments | Reference |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | NA | NA | hetero | 40; 46 | NA | 40 | I | personal or family history of Other VTE | NA | Finland | thrombosis (Other VTE) | PMID: 16360797 |
| Mutation type:Point | Mutation effect:Missense | Nucleotide number:318 | |||
| Genome location:Exon5 | Subdomain:EGF1 | ||||
| Alpha missense prediction value:0.9044 | Alpha missense prediction class:pathogenic | ||||
| No. of patients reported: 2 | |||||
| Patient information: Monoallelic variation (2); Biallelic variation (0) | |||||
| Patient | Sex | Age | Genotype | PC: amidolytic act (%) | PC: clotting act (%) | PC: Ag (%) | PCD type | Clinical presentation (age) | First onset age | Country | Comments | Reference |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | M | NA | hetero | NA | NA | 50 | I | asymptomatic | NA | China | NA | PMID: 16689777 |
| 2 | F | 32 | hetero | NA | NA | NA | I | Other VTE, DVT, died of Other VTE | 32 | China | MVT (Other VTE); disseminated thrombosis (Other VTE) | PMID: 16689777 |
| Mutation type:Point; Point | Mutation effect:Missense; Missense | Nucleotide number:318; 541 | |||
| Genome location:Exon5; Exon7 | Subdomain:EGF1; Linker | ||||
| Alpha missense prediction value:0.9044; 0.4146 | Alpha missense prediction class:pathogenic; ambiguous | ||||
| No. of patients reported: 1 | |||||
| Patient information: Monoallelic variation (0); Biallelic variation (1) | |||||
| Patient | Sex | Age | Genotype | PC: amidolytic act (%) | PC: clotting act (%) | PC: Ag (%) | PCD type | Clinical presentation (age) | First onset age | Country | Comments | Reference |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | F | 32 | c.hetero | 1.2 | NA | 1 | I | DVT (24, 30), Other VTE (30) | 24 | China | thrombosis (Other VTE) | PMID: 16689777 |