Search Results: 24 genotypes retrieved

Data download

c.565C>T

p.Arg189Trp
Mutation type:Point Mutation effect:Missense Nucleotide number:565
Genome location:Exon7 Subdomain:Linker
Alpha missense prediction value:0.0952 Alpha missense prediction class:benign
No. of patients reported: 279
Patient information: Monoallelic variation (279); Biallelic variation (0)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 NA NA hetero 44 NA NA NA Other VTE 48 USA thrombosis (Other VTE) PMID: 8972002
2 NA NA hetero NA NA NA NA asymptomatic NA USA NA PMID: 8972002
3 NA NA hetero NA NA NA NA asymptomatic NA USA NA PMID: 8972002
4 NA NA hetero NA NA NA NA asymptomatic NA USA NA PMID: 8972002
5 NA NA hetero NA NA NA NA asymptomatic NA USA NA PMID: 8972002
6 NA NA hetero NA NA NA II asymptomatic NA China NA PMID: 37950050
7 F 49 hetero 43 NA 77 II PE, DVT (49, died later), lung cancer 49 China NA PMID: 37950050
8 M NA hetero NA NA NA II lung cancer NA China NA PMID: 37950050
9 M NA hetero NA NA NA II stroke NA China NA PMID: 37950050
10 F 25 hetero 48 NA 80 II asymptomatic 25 China pregnancy PMID: 37950050
11 NA NA hetero NA NA NA II asymptomatic NA China NA PMID: 37950050
12 F 64 hetero 51 NA 73 II DVT 64 China NA PMID: 37950050
13 F NA hetero NA NA NA II DVT NA China NA PMID: 37950050
14 NA NA hetero NA NA NA II asymptomatic NA China NA PMID: 37950050
15 NA NA hetero NA NA NA II asymptomatic NA China NA PMID: 37950050
16 NA NA hetero NA NA NA II asymptomatic NA China NA PMID: 37950050
17 NA NA hetero NA NA NA II asymptomatic NA China NA PMID: 37950050
18 M 53 hetero 50 NA 75 II DVT (53) 53 China NA PMID: 37950050
19 NA NA hetero NA NA NA II asymptomatic NA China NA PMID: 37950050
20 NA NA hetero NA NA NA II asymptomatic NA China NA PMID: 37950050
21 M 29 hetero NA NA NA NA PE (27, 29) 27 China NA PMID: 37789321
22 F NA hetero NA NA NA NA NA NA China NA PMID: 37789321
23 M 34 hetero NA NA NA NA multiple DVT and PE (32) 32 China NA PMID: 37789321
24 M NA hetero NA NA NA NA NA NA China NA PMID: 37789321
25 M 38 hetero NA NA NA NA Other VTE (31, 35) 31 China PVT (Other VTE) PMID: 37789321
26 M NA hetero NA NA NA NA NA NA China NA PMID: 37789321
27 F 26 hetero NA NA NA NA DVT and PE (21) 21 China NA PMID: 37789321
28 M NA hetero NA NA NA NA NA NA China NA PMID: 37789321
29 F 65 hetero NA NA NA NA DVT and PE (61) 61 China NA PMID: 37789321
30 M 32 hetero NA NA NA NA Other VTE (31) 31 China CVT (Other VTE) PMID: 37789321
31 F NA hetero NA NA NA NA NA NA China NA PMID: 37789321
32 F 37 hetero NA NA NA NA DVT (36) 36 China NA PMID: 37789321
33 F 27 hetero NA NA NA NA PE (26) 26 China pregnancy PMID: 37789321
34 M NA hetero NA NA NA NA NA NA China NA PMID: 37789321
35 F NA hetero NA NA NA NA NA NA China NA PMID: 37789321
36 M NA hetero NA NA NA NA NA NA China NA PMID: 37789321
37 F NA hetero NA NA NA NA NA NA China NA PMID: 37789321
38 F NA hetero NA NA NA NA NA NA China NA PMID: 37789321
39 M NA hetero NA NA NA NA NA NA China NA PMID: 37789321
40 M 35 hetero NA NA NA NA MI (26), PE, DVT (44) 26 China PSD (p.E67A); sedentariness 1st PMID: 37789321
41 M 38 hetero NA NA NA NA Other VTE (36) 36 China PVT (Other VTE); PSD (R561W) PMID: 37789321
42 M NA hetero NA NA NA NA NA NA China NA PMID: 37789321
43 M 46 hetero NA NA NA NA PE (38), stroke (40) 38 China PLG (Exon1-2deletion) PMID: 37789321
44 M 32 hetero NA NA NA NA DVT (30) 30 China hyperlipidemia; Klinefelter syndrome PMID: 37789321
45 M NA hetero NA NA NA NA NA NA China NA PMID: 37789321
46 M 53 hetero 50 NA 75 II DVT 53 China Smoking PMID: 35231991
47 NA NA hetero 64.1 58 61.3 IIb Other VTE NA France NA PMID: 32717757
48 NA NA hetero 64.1 58 61.3 IIb Other VTE NA France NA PMID: 32717757
49 NA NA hetero 64.1 58 61.3 IIb Other VTE NA France NA PMID: 32717757
50 NA NA hetero 64.1 58 61.3 IIb Other VTE NA France NA PMID: 32717757
51 NA NA hetero 64.1 58 61.3 IIb Other VTE NA France NA PMID: 32717757
52 NA NA hetero 64.1 58 61.3 IIb Other VTE NA France NA PMID: 32717757
53 NA NA hetero 64.1 58 61.3 IIb Other VTE NA France NA PMID: 32717757
54 NA NA hetero 64.1 58 61.3 IIb Other VTE NA France NA PMID: 32717757
55 NA NA hetero 64.1 58 61.3 IIb Other VTE NA France NA PMID: 32717757
56 NA NA hetero 64.1 58 61.3 IIb Other VTE NA France NA PMID: 32717757
57 NA NA hetero 64.1 58 61.3 IIb asymptomatic NA France NA PMID: 32717757
58 NA NA hetero 64.1 58 61.3 IIb asymptomatic NA France NA PMID: 32717757
59 NA NA hetero 64.1 58 61.3 IIb asymptomatic NA France NA PMID: 32717757
60 NA NA hetero 64.1 58 61.3 IIb asymptomatic NA France NA PMID: 32717757
61 NA NA hetero 64.1 58 61.3 IIb asymptomatic NA France NA PMID: 32717757
62 NA NA hetero 64.1 58 61.3 IIb asymptomatic NA France NA PMID: 32717757
63 NA NA hetero 64.1 58 61.3 IIb asymptomatic NA France NA PMID: 32717757
64 NA NA hetero 64.1 58 61.3 IIb asymptomatic NA France NA PMID: 32717757
65 NA NA hetero 64.1 58 61.3 IIb asymptomatic NA France NA PMID: 32717757
66 NA NA hetero 64.1 58 61.3 IIb asymptomatic NA France NA PMID: 32717757
67 F 25 hetero 62.75 NA <70 NA asymptomatic 25 Thailand NA PMID: 30925296
68 M 23 hetero 62.75 NA <70 NA asymptomatic 23 Thailand NA PMID: 30925296
69 F 35 hetero 68.75 NA <70 NA asymptomatic 35 Thailand NA PMID: 30925296
70 F 35 hetero NA NA 57.6 NA stroke (35, recurrent), Other VTE (31), SLE, hyperthyroidism (31) 31 China thrombosis (Other VTE); antiplatelet agent aspirin PMID: 30210609
71 M NA hetero NA NA NA NA asymptomatic NA China NA PMID: 30210609
72 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
73 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
74 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
75 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
76 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
77 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
78 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
79 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
80 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
81 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
82 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
83 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
84 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
85 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
86 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
87 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
88 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
89 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
90 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
91 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
92 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
93 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
94 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
95 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
96 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
97 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
98 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
99 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
100 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
101 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
102 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
103 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
104 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
105 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
106 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
107 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
108 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
109 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
110 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
111 NA NA hetero 80.0 (37-168) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
112 NA ≤18 hetero 80.0 (37-168) NA NA NA Arterial ischemic stroke ≤18 Thailand NA PMID: 28511552
113 NA ≤18 hetero 80.0 (37-168) NA NA NA Arterial ischemic stroke ≤18 Thailand NA PMID: 28511552
114 NA ≤18 hetero 80.0 (37-168) NA NA NA Arterial ischemic stroke ≤18 Thailand NA PMID: 28511552
115 NA ≤18 hetero 80.0 (37-168) NA NA NA Arterial ischemic stroke ≤18 Thailand NA PMID: 28511552
116 NA ≤18 hetero 80.0 (37-168) NA NA NA Arterial ischemic stroke ≤18 Thailand NA PMID: 28511552
117 NA ≤18 hetero 80.0 (37-168) NA NA NA Arterial ischemic stroke ≤18 Thailand NA PMID: 28511552
118 NA ≤18 hetero 80.0 (37-168) NA NA NA Other VTE ≤18 Thailand NA PMID: 28511552
119 NA ≤18 hetero 80.0 (37-168) NA NA NA Other VTE ≤18 Thailand NA PMID: 28511552
120 NA ≤18 hetero 80.0 (37-168) NA NA NA Other VTE ≤18 Thailand NA PMID: 28511552
121 NA ≤18 hetero 80.0 (37-168) NA NA NA Other VTE ≤18 Thailand NA PMID: 28511552
122 NA ≤18 hetero 80.0 (37-168) NA NA NA Other VTE ≤18 Thailand NA PMID: 28511552
123 NA ≤18 hetero 80.0 (37-168) NA NA NA Other VTE ≤18 Thailand NA PMID: 28511552
124 NA ≤18 hetero 80.0 (37-168) NA NA NA Other VTE ≤18 Thailand CVT (Other VTE) PMID: 28511552
125 NA ≤18 hetero 80.0 (37-168) NA NA NA Other VTE ≤18 Thailand CVT (Other VTE) PMID: 28511552
126 NA ≤18 hetero 80.0 (37-168) NA NA NA Other VTE ≤18 Thailand CVT (Other VTE) PMID: 28511552
127 NA ≤18 hetero 80.0 (37-168) NA NA NA Other VTE ≤18 Thailand CVT (Other VTE) PMID: 28511552
128 NA ≤18 hetero 80.0 (37-168) NA NA NA Other VTE ≤18 Thailand CVT (Other VTE) PMID: 28511552
129 NA ≤18 hetero 80.0 (37-168) NA NA NA Systemic AT ≤18 Thailand NA PMID: 28511552
130 M 35 hetero 69 NA 78 II asymptomatic 35 China NA PMID: 28186585
131 F 41 hetero 65 NA 76 II asymptomatic 41 China NA PMID: 28186585
132 M 53 hetero 50 NA 75 II Other VTE 53 China long-term smoking PMID: 28186585
133 M 29 hetero 64 NA 82 II asymptomatic 29 China NA PMID: 28186585
134 M NA hetero 60 NA 79 NA asymptomatic NA China NA PMID: 27314862
135 F NA hetero 61 NA 76 NA asymptomatic NA China NA PMID: 27314862
136 NA NA hetero 45.6 NA NA NA DVT, recurrent Other VTE NA China familly history of VTE PMID: 24028705
137 NA NA hetero 63.9 NA NA NA DVT NA China NA PMID: 24028705
138 NA NA hetero 77.6 NA NA NA DVT NA China NA PMID: 24028705
139 NA NA hetero 46.8 NA NA NA DVT NA China NA PMID: 24028705
140 NA NA hetero 26.2 NA NA NA DVT NA China NA PMID: 24028705
141 M 24 hetero 46 NA 64.4 NA PE (22), DVT (22, 24) 22 China PSD (Tyr519X), family history of DVT PMID: 22951146
142 F 24 hetero 65.9 NA 76.5 NA DVT (21) 21 China NA PMID: 22951146
143 F 24 hetero 38.6 NA 45.3 NA DVT (23, 24) 23 China NA PMID: 22951146
144 F 33 hetero 63.9 NA 71.8 NA DVT (33) 33 China Pregnancy PMID: 22951146
145 M 19 hetero 69.4 NA 74.9 NA DVT (19) 19 China NA PMID: 22951146
146 M 68 hetero 46.8 NA 67.2 NA DVT and PE (68) 68 China surgery PMID: 22951146
147 M 28 hetero 63.9 NA 64 NA DVT (28) 28 China NA PMID: 22951146
148 F 24 hetero 65.9 NA NA NA Other VTE 24 China NA PMID: 22944127
149 M 24 hetero 38.6 NA NA NA Other VTE 24 China NA PMID: 22944127
150 F 33 hetero 63.9 NA NA NA Other VTE 33 China NA PMID: 22944127
151 M 19 hetero 61 NA NA NA Other VTE 19 China NA PMID: 22944127
152 M 68 hetero 46.8 NA NA NA Other VTE 68 China NA PMID: 22944127
153 M 28 hetero 26.2 NA NA NA Other VTE 28 China NA PMID: 22944127
154 F 26 hetero 63 NA 65 I DVT 26 India NA PMID: 22576310
155 M 46 hetero 46 NA 48 I DVT 46 India NA PMID: 22576310
156 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
157 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
158 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
159 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
160 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
161 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
162 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
163 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
164 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
165 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
166 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
167 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
168 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
169 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
170 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
171 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
172 NA NA hetero 40.4-62.3 NA 68.7-83.0 II DVT NA China NA PMID: 22545135
173 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
174 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
175 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
176 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
177 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
178 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
179 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
180 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
181 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
182 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
183 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
184 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
185 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
186 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
187 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
188 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
189 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
190 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
191 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
192 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
193 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
194 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
195 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
196 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
197 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
198 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
199 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
200 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
201 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
202 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
203 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
204 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
205 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
206 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
207 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
208 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
209 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
210 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
211 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
212 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
213 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
214 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
215 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
216 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
217 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
218 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
219 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
220 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
221 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
222 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
223 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
224 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
225 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
226 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
227 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
228 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
229 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
230 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
231 NA NA hetero 40.4-62.3 NA 68.7-83.0 II Other VTE NA China NA PMID: 22545135
232 NA NA hetero 40.4-62.3 NA 68.7-83.0 II asymptomatic NA China NA PMID: 22545135
233 NA NA hetero 40.4-62.3 NA 68.7-83.0 II asymptomatic NA China NA PMID: 22545135
234 NA NA hetero 40.4-62.3 NA 68.7-83.0 II asymptomatic NA China NA PMID: 22545135
235 NA NA hetero 40.4-62.3 NA 68.7-83.0 II asymptomatic NA China NA PMID: 22545135
236 NA NA hetero 40.4-62.3 NA 68.7-83.0 II asymptomatic NA China NA PMID: 22545135
237 NA NA hetero 40.4-62.3 NA 68.7-83.0 II asymptomatic NA China NA PMID: 22545135
238 NA NA hetero 40.4-62.3 NA 68.7-83.0 II asymptomatic NA China NA PMID: 22545135
239 NA NA hetero 40.4-62.3 NA 68.7-83.0 II asymptomatic NA China NA PMID: 22545135
240 NA NA hetero 40.4-62.3 NA 68.7-83.0 II asymptomatic NA China NA PMID: 22545135
241 NA NA hetero 40.4-62.3 NA 68.7-83.0 II asymptomatic NA China NA PMID: 22545135
242 NA NA hetero 40.4-62.3 NA 68.7-83.0 II asymptomatic NA China NA PMID: 22545135
243 NA NA hetero 40.4-62.3 NA 68.7-83.0 II asymptomatic NA China NA PMID: 22545135
244 NA NA hetero 40.4-62.3 NA 68.7-83.0 II asymptomatic NA China NA PMID: 22545135
245 F NA hetero 16 NA 83 II asymptomatic NA China NA PMID: 22366017
246 F NA hetero 15 NA 72 II asymptomatic NA China NA PMID: 22366017
247 F 26 hetero NA NA 65 NA DVT (26) 26 India NA PMID: 19350130
248 NA NA hetero 35 NA 49 NA Other VTE (42) 42 China thrombosis (Other VTE) PMID: 15114590
249 NA NA hetero 54 NA 66 NA Other VTE (38) 38 China thrombosis (Other VTE) PMID: 15114590
250 NA NA hetero 44 NA 48 NA Other VTE (75) 75 China thrombosis (Other VTE) PMID: 15114590
251 NA NA hetero 58 NA 78 NA Other VTE (56) 56 China thrombosis (Other VTE) PMID: 15114590
252 NA NA hetero 72 NA 74 NA Other VTE during SLE with nephritis (15) 15 China thrombosis (Other VTE) PMID: 15114590
253 NA NA hetero 65 NA 76 NA Other VTE (29) 29 China thrombosis (Other VTE); PSD PMID: 15114590
254 NA NA hetero 54.7±13.6 NA 54.7±11.5 NA DVT after an operation for brain abscess (43) 43 China surgery PMID: 15114590
255 NA NA hetero 61.8±6.6 NA 65.2±13.5 NA asymptomatic NA China NA PMID: 15114590
256 NA NA hetero 61.8±6.6 NA 65.2±13.5 NA asymptomatic NA China NA PMID: 15114590
257 NA NA hetero 61.8±6.6 NA 65.2±13.5 NA asymptomatic NA China NA PMID: 15114590
258 NA NA hetero 61.8±6.6 NA 65.2±13.5 NA asymptomatic NA China NA PMID: 15114590
259 NA NA hetero 61.8±6.6 NA 65.2±13.5 NA asymptomatic NA China NA PMID: 15114590
260 NA NA hetero 61.8±6.6 NA 65.2±13.5 NA asymptomatic NA China NA PMID: 15114590
261 NA NA hetero 61.8±6.6 NA 65.2±13.5 NA asymptomatic NA China NA PMID: 15114590
262 NA NA hetero 61.8±6.6 NA 65.2±13.5 NA asymptomatic NA China NA PMID: 15114590
263 NA NA hetero 61.8±6.6 NA 65.2±13.5 NA asymptomatic NA China NA PMID: 15114590
264 NA NA hetero 61.8±6.6 NA 65.2±13.5 NA asymptomatic NA China NA PMID: 15114590
265 NA NA hetero 61.8±6.6 NA 65.2±13.5 NA asymptomatic NA China NA PMID: 15114590
266 NA NA hetero NA NA NA NA asymptomatic NA China NA PMID: 15114590
267 NA NA hetero NA NA NA NA asymptomatic NA China NA PMID: 15114590
268 NA NA hetero NA NA NA NA asymptomatic NA China NA PMID: 15114590
269 NA NA hetero NA NA NA NA asymptomatic NA China NA PMID: 15114590
270 NA NA hetero NA NA NA NA asymptomatic NA China NA PMID: 15114590
271 NA NA hetero NA NA NA NA asymptomatic NA China NA PMID: 15114590
272 NA NA hetero NA NA NA NA asymptomatic NA China NA PMID: 15114590
273 NA NA hetero NA NA NA NA asymptomatic NA China NA PMID: 15114590
274 NA NA hetero NA NA NA NA asymptomatic NA China NA PMID: 15114590
275 NA NA hetero NA NA NA NA asymptomatic NA China NA PMID: 15114590
276 NA NA hetero NA NA NA NA asymptomatic NA China NA PMID: 15114590
277 NA NA hetero 49 NA 45 I NA NA UK NA PMID: 7482420
278 NA NA hetero 73 NA 74 I NA NA Netherlands NA PMID: 7482420
279 NA NA hetero NA NA NA NA NA NA USA NA PMID: 7482420

c.566G>A

p.Arg189Gln
Mutation type:Point Mutation effect:Missense Nucleotide number:566
Genome location:Exon7 Subdomain:Linker
Alpha missense prediction value:0.0783 Alpha missense prediction class:benign
No. of patients reported: 5
Patient information: Monoallelic variation (5); Biallelic variation (0)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 21 hetero 26 NA 70 II Other VTE with peri-venous panniculitis (21) 21 Japan apixaban, urokinase and unfractionated heparin PMID: 36312771
2 F 84 hetero 83 NA 123 II NA NA Japan NA PMID: 36312771
3 F 47 hetero 98 NA 165 II NA NA Japan NA PMID: 36312771
4 M 23 hetero <10 NA 33 II Other VTE (20) 20 Japan anticoagulation therapy PMID: 36312771
5 F 19 hetero 20 NA 90 II NA NA Japan NA PMID: 36312771

c.[565C>T]; [565C>T]

p.[Arg189Trp]; [Arg189Trp]
Mutation type:Point; Point Mutation effect:Missense; Missense Nucleotide number:565; 565
Genome location:Exon7; Exon7 Subdomain:Linker; Linker
Alpha missense prediction value:0.0952; 0.0952 Alpha missense prediction class:benign; benign
No. of patients reported: 15
Patient information: Monoallelic variation (0); Biallelic variation (15)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 F 42 homo 44 NA 56 I Infertility 42 China NA PMID: 37950050
2 F 46 homo 28 NA 78 II Other VTE (46) 46 China CVT (Other VTE) PMID: 37950050
3 F 46 homo 21 NA 53 I Other VTE (46) 46 China CVT (Other VTE) PMID: 37950050
4 F 46 homo 21 NA 78 II Other VTE (46) 46 China CVT (Other VTE); consanguineous marriage PMID: 35231991
5 F 45 homo 48 NA <70 NA asymptomatic 45 Thailand NA PMID: 30925296
6 F 22 homo 49.5 NA <70 NA asymptomatic 22 Thailand NA PMID: 30925296
7 F 22 homo 41.5 NA <70 NA asymptomatic 22 Thailand NA PMID: 30925296
8 F 32 homo 54 NA <70 NA asymptomatic 32 Thailand NA PMID: 30925296
9 M 66 homo 49.5 NA <70 NA asymptomatic 66 Thailand NA PMID: 30925296
10 NA NA homo 44.3 (14.4-73.1) NA NA NA asymptomatic NA Thailand NA PMID: 28511552
11 NA ≤18 homo 44.3 (14.4-73.1) NA NA NA acute ischemic stroke ≤18 Thailand NA PMID: 28511552
12 NA ≤18 homo 44.3 (14.4-73.1) NA NA NA acute ischemic stroke ≤18 Thailand NA PMID: 28511552
13 NA ≤18 homo 44.3 (14.4-73.1) NA NA NA acute ischemic stroke ≤18 Thailand NA PMID: 28511552
14 NA ≤18 homo 44.3 (14.4-73.1) NA NA NA Other VTE ≤18 Thailand NA PMID: 28511552
15 NA ≤18 homo 44.3 (14.4-73.1) NA NA NA Other VTE ≤18 Thailand NA PMID: 28511552

c.[-228T>C]; [565C>T]

NA; p.Arg189Trp
Mutation type:Point; Point Mutation effect:Gene expression; Missense Nucleotide number:-228; 565
Genome location:Promoter; Exon7 Subdomain:NA; Linker
Alpha missense prediction value:0.0952 Alpha missense prediction class:benign
No. of patients reported: 3
Patient information: Monoallelic variation (0); Biallelic variation (3)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 33 c.hetero 61 NA <70 NA asymptomatic 33 Thailand NA PMID: 30925296
2 F 26 c.hetero 65 NA <70 NA asymptomatic 26 Thailand NA PMID: 30925296
3 F 40 c.hetero 57.75 NA <70 NA asymptomatic 40 Thailand NA PMID: 30925296

c.[66T>C]; [565C>T]

p.[Pro22pro]; [Arg189Trp]
Mutation type:Point; Point Mutation effect:Silent; Missense Nucleotide number:66; 565
Genome location:Exon2; Exon7 Subdomain:Propeptide; Linker
Alpha missense prediction value:0.0952 Alpha missense prediction class:benign
No. of patients reported: 1
Patient information: Monoallelic variation (0); Biallelic variation (1)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 NA NA c.hetero NA NA NA NA Other VTE NA France thrombosis (Other VTE) PMID: 10669160

c.[76G>A]; [565C>T]

p.[Val26Met]; [Arg189Trp]
Mutation type:Point; Point Mutation effect:Missense; Missense Nucleotide number:76; 565
Genome location:Exon3; Exon7 Subdomain:Propeptide; Linker
Alpha missense prediction value:0.3205; 0.0952 Alpha missense prediction class:benign; benign
No. of patients reported: 1
Patient information: Monoallelic variation (0); Biallelic variation (1)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 48 c.hetero NA NA PC defect I DVT, PE (48) 48 China NA PMID: 37789321

c.[169C>T]; [565C>T]

p.[Arg57Trp]; [Arg189Trp]
Mutation type:Point; Point Mutation effect:Missense; Missense Nucleotide number:169; 565
Genome location:Exon3; Exon7 Subdomain:Gla; Linker
Alpha missense prediction value:0.3331; 0.0952 Alpha missense prediction class:benign; benign
No. of patients reported: 1
Patient information: Monoallelic variation (0); Biallelic variation (1)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 27 c.hetero 39 NA 42.1 NA DVT (25, 26) 25 China NA PMID: 22951146

c.[211G>A]; [565C>T]

p.[Glu71Lys]; [Arg189Trp]
Mutation type:Point; Point Mutation effect:Missense; Missense Nucleotide number:211; 565
Genome location:Exon3; Exon7 Subdomain:Gla; Linker
Alpha missense prediction value:0.6691; 0.0952 Alpha missense prediction class:pathogenic; benign
No. of patients reported: 2
Patient information: Monoallelic variation (0); Biallelic variation (2)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 20 c.hetero 19 NA 42 NA PE (19) 19 China NA PMID: 22951146
2 M 19 c.hetero 19 NA 42 II PE 19 China LMWH, thrombolysis, anticoagulation therapy PMID: 22366017

c.[247T>C]; [565C>T]

p.[Trp83Arg]; [Arg189Trp]
Mutation type:Point; Point Mutation effect:Missense; Missense Nucleotide number:247; 565
Genome location:Exon4; Exon7 Subdomain:Gla; Linker
Alpha missense prediction value:0.9123; 0.0952 Alpha missense prediction class:pathogenic; benign
No. of patients reported: 1
Patient information: Monoallelic variation (0); Biallelic variation (1)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 54 c.hetero NA NA PC defect NA Other VTE (34); DVT (50) 34 China thrombosis (Other VTE) PMID: 37789321

c.[262+2T>C]; [565C>T]

NA; p.Arg189Trp
Mutation type:Point; Point Mutation effect:Splice; Missense Nucleotide number:262; 565
Genome location:Intron4; Exon7 Subdomain:NA; Linker
Alpha missense prediction value:0.0952 Alpha missense prediction class:benign
No. of patients reported: 1
Patient information: Monoallelic variation (0); Biallelic variation (1)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 35 c.hetero 53 NA PC defect NA multiple DVT (29) 29 China NA PMID: 37789321

c.[325G>C]; [565C>T]

p.[Gly109Arg]; [Arg189Trp]
Mutation type:Point; Point Mutation effect:Missense; Missense Nucleotide number:325; 565
Genome location:Exon5; Exon7 Subdomain:EGF1; Linker
Alpha missense prediction value:0.8221; 0.0952 Alpha missense prediction class:pathogenic; benign
No. of patients reported: 1
Patient information: Monoallelic variation (0); Biallelic variation (1)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 49 c.hetero NA NA PC defect I PE (47) 47 China NA PMID: 37789321

c.[383G>A]; [565C>T]

p.[Gly128Asp]; [Arg189Trp]
Mutation type:Point; Point Mutation effect:Missense; Missense Nucleotide number:383; 565
Genome location:Exon5; Exon7 Subdomain:EGF1; Linker
Alpha missense prediction value:0.6093; 0.0952 Alpha missense prediction class:pathogenic; benign
No. of patients reported: 4
Patient information: Monoallelic variation (0); Biallelic variation (4)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 8 c.hetero 30 NA 35 I PF (8) 8 China NA PMID: 37950050
2 M 8 c.hetero 18 NA 58 I PF (8) 8 China NA PMID: 35231991
3 M 8 c.hetero 30 NA 35 I PF 8 China NA PMID: 28186585
4 M 12 c.hetero 27 NA 35 I asymptomatic 12 China NA PMID: 27314862

c.[541T>G]; [565C>T]

p.[Phe181Val]; [Arg189Trp]
Mutation type:Point; Point Mutation effect:Missense; Missense Nucleotide number:541; 565
Genome location:Exon7; Exon7 Subdomain:Linker; Linker
Alpha missense prediction value:0.4146; 0.0952 Alpha missense prediction class:ambiguous; benign
No. of patients reported: 1
Patient information: Monoallelic variation (0); Biallelic variation (1)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 24 c.hetero NA NA PC defect I DVT (14, 22, 23), APS 14 China NA PMID: 37789321

c.[565C>T]; [1081A>G]

p.[Arg189Trp]; [Asn361Asp]
Mutation type:Point; Point Mutation effect:Missense; Missense Nucleotide number:565; 1081
Genome location:Exon7; Exon9 Subdomain:Linker; Serine protease
Alpha missense prediction value:0.0952; 0.2464 Alpha missense prediction class:benign; benign
No. of patients reported: 1
Patient information: Monoallelic variation (0); Biallelic variation (1)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 F 34 c.hetero 58 NA PC defect NA Other VTE (31) 31 China PVT (Other VTE); Oral contraceptives PMID: 37789321

c.[565C>T]; [1115A>G]

p.[Arg189Trp]; [Glu372Gly]
Mutation type:Point; Point Mutation effect:Missense; Missense Nucleotide number:565; 1115
Genome location:Exon7; Exon9 Subdomain:Linker; Serine protease
Alpha missense prediction value:0.0952; 0.2224 Alpha missense prediction class:benign; benign
No. of patients reported: 1
Patient information: Monoallelic variation (0); Biallelic variation (1)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 31 c.hetero 49 NA PC defect NA DVT (27, 30) 27 China sedentariness 1st PMID: 37789321

c.[565C>T]; [1130T>C]

p.[Arg189Trp]; [Met377Thr]
Mutation type:Point; Point Mutation effect:Missense; Missense Nucleotide number:565; 1130
Genome location:Exon7; Exon9 Subdomain:Linker; Serine protease
Alpha missense prediction value:0.0952; 0.7544 Alpha missense prediction class:benign; pathogenic
No. of patients reported: 1
Patient information: Monoallelic variation (0); Biallelic variation (1)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 33 c.hetero NA NA PC defect I DVT, PE (29) 29 China NA PMID: 37789321

c.[565C>T]; [1139_1145delTGGTGTC]

p.[Arg189Trp]; [Val381ArgfsX38]
Mutation type:Point; Deletion Mutation effect:Missense; Frameshift Nucleotide number:565; 1139
Genome location:Exon7; Exon9 Subdomain:Linker; Serine protease
Alpha missense prediction value:0.0952 Alpha missense prediction class:benign
No. of patients reported: 1
Patient information: Monoallelic variation (0); Biallelic variation (1)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 69 c.hetero 45 NA PC defect NA DVT (51, 60, 66) 51 China surgery 2nd PMID: 37789321

c.[565C>T]; [1157T>C]

p.[Arg189Trp]; [Leu386Pro]
Mutation type:Point; Point Mutation effect:Missense; Missense Nucleotide number:565; 1157
Genome location:Exon7; Exon9 Subdomain:Linker; Serine protease
Alpha missense prediction value:0.0952; 0.9891 Alpha missense prediction class:benign; pathogenic
No. of patients reported: 1
Patient information: Monoallelic variation (0); Biallelic variation (1)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 58 c.hetero NA NA PC defect NA DVT, PE (42, 56) 42 China NA PMID: 37789321

c.[565C>T]; [1212delG]

p.[Arg189Trp]; [Met406TrpfsX15]
Mutation type:Point; Deletion Mutation effect:Missense; Frameshift Nucleotide number:565; 1212
Genome location:Exon7; Exon9 Subdomain:Linker; Serine protease
Alpha missense prediction value:0.0952 Alpha missense prediction class:benign
No. of patients reported: 1
Patient information: Monoallelic variation (0); Biallelic variation (1)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 NA NA c.hetero NA 16 26 I Other VTE NA USA thrombosis (Other VTE) PMID: 7482420

c.[565C>T]; [574_576delAAG]

p.[Arg189Trp]; [Lys192del]
Mutation type:Point; Deletion Mutation effect:Missense; Inframe Nucleotide number:565; 574
Genome location:Exon7; Exon7 Subdomain:Linker; Linker
Alpha missense prediction value:0.0952 Alpha missense prediction class:benign
No. of patients reported: 6
Patient information: Monoallelic variation (0); Biallelic variation (6)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 38 c.hetero NA NA PC defect NA multiple DVT (34) 34 China Surgery PMID: 37789321
2 M 54 c.hetero NA NA PC defect NA DVT (48, 53), PE (53) 48 China NA PMID: 37789321
3 M 38 c.hetero NA NA PC defect NA multiple DVT (34) 34 China NA PMID: 37789321
4 M 54 c.hetero NA NA PC defect NA DVT (48, 53), PE (53) 48 China NA PMID: 37789321
5 F NA c.hetero 41 NA NA NA DVT NA Korea NA PMID: 24162787
6 NA NA c.hetero 56 NA 60 NA Other VTE (41) 41 China thrombosis (Other VTE) PMID: 15114590

c.[565C>T]; [632G>A]

p.[Arg189Trp]; [Arg211Gln]
Mutation type:Point; Point Mutation effect:Missense; Missense Nucleotide number:565; 632
Genome location:Exon7; Exon7 Subdomain:Linker; Activation peptide
Alpha missense prediction value:0.0952; 0.144 Alpha missense prediction class:benign; benign
No. of patients reported: 1
Patient information: Monoallelic variation (0); Biallelic variation (1)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 33 c.hetero NA NA PC defect NA multiple DVT (23, 24, 31) 23 China Trauma 1st PMID: 37789321

c.[565C>T]; [658C>T]

p.[Arg189Trp]; [Arg220Trp]
Mutation type:Point; Point Mutation effect:Missense; Missense Nucleotide number:565; 658
Genome location:Exon7; Exon7 Subdomain:Linker; Serine protease
Alpha missense prediction value:0.0952; 0.0663 Alpha missense prediction class:benign; benign
No. of patients reported: 4
Patient information: Monoallelic variation (0); Biallelic variation (4)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 M 56 c.hetero NA NA PC defect I multiple DVT (49, 54) 49 China NA PMID: 37789321
2 M 26 c.hetero NA NA PC defect I stroke (21) 21 China NA PMID: 37789321
3 M 47 c.hetero 30 NA 48.4 I DVT (40, 43) 40 China Cholecystectomy PMID: 22951146
4 M NA c.hetero NA NA NA I DVT NA China NA PMID: 22951146

c.[565C>T]; [743T>C]

p.[Arg189Trp]; [Val248Ala]
Mutation type:Point; Point Mutation effect:Missense; Missense Nucleotide number:565; 743
Genome location:Exon7; Exon8 Subdomain:Linker; Serine protease
Alpha missense prediction value:0.0952; 0.5727 Alpha missense prediction class:benign; pathogenic
No. of patients reported: 1
Patient information: Monoallelic variation (0); Biallelic variation (1)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 NA NA c.hetero 37 NA 53 NA Other VTE (44) 44 China thrombosis (Other VTE); Oral pill for 10 years+long airline flight PMID: 15114590

c.[565C>T]; [815G>A; 889G>C]

p.[Arg189Trp]; [Arg272His; Asp297His]
Mutation type:Point; Point; Point Mutation effect:Missense; Missense; Missense Nucleotide number:565; 815; 889
Genome location:Exon7; Exon9; Exon9 Subdomain:Linker; Serine protease; Serine protease
Alpha missense prediction value:0.0952; 0.1052; 0.735 Alpha missense prediction class:benign; benign; pathogenic
No. of patients reported: 1
Patient information: Monoallelic variation (0); Biallelic variation (1)
Patient Sex Age Genotype PC: amidolytic act (%) PC: clotting act (%) PC: Ag (%) PCD type Clinical presentation (age) First onset age Country Comments Reference
1 NA NA c.hetero 16 NA 42 NA Other VTE (14) 14 China thrombosis (Other VTE) PMID: 15114590