| Mutation type:Point | Mutation effect:Missense | Nucleotide number:76 | |||
| Genome location:Exon3 | Subdomain:Propeptide | ||||
| Alpha missense prediction value:0.3205 | Alpha missense prediction class:benign | ||||
| No. of patients reported: 2 | |||||
| Patient information: Monoallelic variation (2); Biallelic variation (0) | |||||
| Patient | Sex | Age | Genotype | PC: amidolytic act (%) | PC: clotting act (%) | PC: Ag (%) | PCD type | Clinical presentation (age) | First onset age | Country | Comments | Reference |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | NA | NA | hetero | 62 | 60 | 60 | I | edema | NA | Japan | NA | PMID: 9840027 |
| 2 | F | NA | hetero | NA | NA | NA | I | NA | NA | China | NA | PMID: 37789321 |
| Mutation type:Point; Point | Mutation effect:Missense; Missense | Nucleotide number:76; 479 | |||
| Genome location:Exon3; Exon6 | Subdomain:Propeptide; EGF2 | ||||
| Alpha missense prediction value:0.3205; 0.9503 | Alpha missense prediction class:benign; pathogenic | ||||
| No. of patients reported: 1 | |||||
| Patient information: Monoallelic variation (0); Biallelic variation (1) | |||||
| Patient | Sex | Age | Genotype | PC: amidolytic act (%) | PC: clotting act (%) | PC: Ag (%) | PCD type | Clinical presentation (age) | First onset age | Country | Comments | Reference |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | NA | NA | c.hetero | NA | NA | NA | I | Other VTE | NA | USA | thrombosis (Other VTE) | PMID: 7482420 |
| Mutation type:Point; Point | Mutation effect:Missense; Missense | Nucleotide number:76; 565 | |||
| Genome location:Exon3; Exon7 | Subdomain:Propeptide; Linker | ||||
| Alpha missense prediction value:0.3205; 0.0952 | Alpha missense prediction class:benign; benign | ||||
| No. of patients reported: 1 | |||||
| Patient information: Monoallelic variation (0); Biallelic variation (1) | |||||
| Patient | Sex | Age | Genotype | PC: amidolytic act (%) | PC: clotting act (%) | PC: Ag (%) | PCD type | Clinical presentation (age) | First onset age | Country | Comments | Reference |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | M | 48 | c.hetero | NA | NA | PC defect | I | DVT, PE (48) | 48 | China | NA | PMID: 37789321 |