| Mutation type:Point | Mutation effect:Missense | Nucleotide number:901 | |||
| Genome location:Exon9 | Subdomain:Serine protease | ||||
| Alpha missense prediction value:0.2688 | Alpha missense prediction class:benign | ||||
| No. of patients reported: 1 | |||||
| Patient information: Monoallelic variation (1); Biallelic variation (0) | |||||
| Patient | Sex | Age | Genotype | PC: amidolytic act (%) | PC: clotting act (%) | PC: Ag (%) | PCD type | Clinical presentation (age) | First onset age | Country | Comments | Reference |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | NA | NA | hetero | NA | NA | NA | NA | Other VTE | NA | France | thrombosis (Other VTE) | PMID: 10669160 |
| Mutation type:Point | Mutation effect:Missense | Nucleotide number:901 | |||
| Genome location:Exon9 | Subdomain:Serine protease | ||||
| Alpha missense prediction value:0.5257 | Alpha missense prediction class:ambiguous | ||||
| No. of patients reported: 1 | |||||
| Patient information: Monoallelic variation (1); Biallelic variation (0) | |||||
| Patient | Sex | Age | Genotype | PC: amidolytic act (%) | PC: clotting act (%) | PC: Ag (%) | PCD type | Clinical presentation (age) | First onset age | Country | Comments | Reference |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | NA | 20 | hetero | 49 | 46 | 48 | I | asymptomatic | 20 | France | NA | PMID: 32717757 |
| Mutation type:Point | Mutation effect:Missense | Nucleotide number:902 | |||
| Genome location:Exon9 | Subdomain:Serine protease | ||||
| Alpha missense prediction value:0.5988 | Alpha missense prediction class:pathogenic | ||||
| No. of patients reported: 6 | |||||
| Patient information: Monoallelic variation (6); Biallelic variation (0) | |||||
| Patient | Sex | Age | Genotype | PC: amidolytic act (%) | PC: clotting act (%) | PC: Ag (%) | PCD type | Clinical presentation (age) | First onset age | Country | Comments | Reference |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | NA | NA | hetero | NA | NA | NA | I | NA | NA | Qatar | NA | PMID: 7482420; PMID: 1678832 |
| 2 | NA | NA | hetero | NA | NA | NA | I | NA | NA | Qatar | NA | PMID: 7482420; PMID: 1678832 |
| 3 | NA | NA | hetero | NA | NA | NA | I | NA | NA | Qatar | NA | PMID: 7482420; PMID: 1678832 |
| 4 | NA | NA | hetero | NA | NA | NA | I | NA | NA | Qatar | NA | PMID: 7482420; PMID: 1678832 |
| 5 | NA | NA | hetero | NA | NA | NA | I | NA | NA | Qatar | NA | PMID: 7482420; PMID: 1678832 |
| 6 | NA | NA | hetero | NA | NA | NA | I | NA | NA | Qatar | NA | PMID: 7482420; PMID: 1678832 |
| Mutation type:Point; Point | Mutation effect:Missense; Missense | Nucleotide number:902; 902 | |||
| Genome location:Exon9; Exon9 | Subdomain:Serine protease; Serine protease | ||||
| Alpha missense prediction value:0.5988; 0.5988 | Alpha missense prediction class:pathogenic; pathogenic | ||||
| No. of patients reported: 1 | |||||
| Patient information: Monoallelic variation (0); Biallelic variation (1) | |||||
| Patient | Sex | Age | Genotype | PC: amidolytic act (%) | PC: clotting act (%) | PC: Ag (%) | PCD type | Clinical presentation (age) | First onset age | Country | Comments | Reference |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | NA | NA | homo | NA | <5 | <5 | I | recurrent PF and DVT | NA | Qatar | consanguineous marriage | PMID: 7482420; PMID: 1678832 |
| Mutation type:Point; Point | Mutation effect:Missense; Missense | Nucleotide number:901; 1218 | |||
| Genome location:Exon9; Exon9 | Subdomain:Serine protease; Serine protease | ||||
| Alpha missense prediction value:0.5257; 0.8981 | Alpha missense prediction class:ambiguous; pathogenic | ||||
| No. of patients reported: 1 | |||||
| Patient information: Monoallelic variation (0); Biallelic variation (1) | |||||
| Patient | Sex | Age | Genotype | PC: amidolytic act (%) | PC: clotting act (%) | PC: Ag (%) | PCD type | Clinical presentation (age) | First onset age | Country | Comments | Reference |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | F | NA | c.hetero | 7 | NA | NA | I | DVT | NA | Korea | NA | PMID: 24162787 |