| Mutation type:Point | Mutation effect:Missense | Nucleotide number:1010 | |||
| Genome location:Exon9 | Subdomain:Serine protease | ||||
| Alpha missense prediction value:0.2048 | Alpha missense prediction class:benign | ||||
| No. of patients reported: 3 | |||||
| Patient information: Monoallelic variation (3); Biallelic variation (0) | |||||
| Patient | Sex | Age | Genotype | PC: amidolytic act (%) | PC: clotting act (%) | PC: Ag (%) | PCD type | Clinical presentation (age) | First onset age | Country | Comments | Reference |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | M | 70 | hetero | 39 | NA | 36 | I | asymptomatic | 70 | China | NA | PMID: 25393254 |
| 2 | M | 45 | hetero | 44 | NA | 33 | I | asymptomatic | 45 | China | NA | PMID: 25393254 |
| 3 | M | 43 | hetero | 43 | NA | 34 | I | asymptomatic | 43 | China | NA | PMID: 25393254 |
| Mutation type:Point; Point | Mutation effect:Missense; Missense | Nucleotide number:26; 1010 | |||
| Genome location:Exon2; Exon9 | Subdomain:Signal peptide; Serine protease | ||||
| Alpha missense prediction value:0.2143; 0.2048 | Alpha missense prediction class:benign; benign | ||||
| No. of patients reported: 1 | |||||
| Patient information: Monoallelic variation (0); Biallelic variation (1) | |||||
| Patient | Sex | Age | Genotype | PC: amidolytic act (%) | PC: clotting act (%) | PC: Ag (%) | PCD type | Clinical presentation (age) | First onset age | Country | Comments | Reference |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | M | 16 | c.hetero | 21 | NA | 20 | I | DVT (14, 15) | 14 | China | NA | PMID: 25393254 |
| Mutation type:Point | Mutation effect:Missense | Nucleotide number:1009 | |||
| Genome location:Exon9 | Subdomain:Serine protease | ||||
| Alpha missense prediction value:0.225 | Alpha missense prediction class:benign | ||||
| No. of patients reported: 2 | |||||
| Patient information: Monoallelic variation (2); Biallelic variation (0) | |||||
| Patient | Sex | Age | Genotype | PC: amidolytic act (%) | PC: clotting act (%) | PC: Ag (%) | PCD type | Clinical presentation (age) | First onset age | Country | Comments | Reference |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | F | 62 | hetero | NA | NA | NA | NA | DVT (61) | 61 | China | family history of VTE | PMID: 40221599 |
| 2 | M | 31 | hetero | NA | NA | NA | NA | DVT, PE (29, recurrent), Other VTE | 29 | China | CVST (Other VTE). family history of VTE | PMID: 40221599 |